{"id":3843,"date":"2026-06-10T17:02:18","date_gmt":"2026-06-10T23:02:18","guid":{"rendered":"https:\/\/somos-hermanos.mx\/?p=3843"},"modified":"2026-06-10T17:02:18","modified_gmt":"2026-06-10T23:02:18","slug":"enfermedad-de-andrade-causan-sintomas-y-tratamiento","status":"publish","type":"post","link":"https:\/\/somos-hermanos.mx\/index.php\/2026\/06\/10\/enfermedad-de-andrade-causan-sintomas-y-tratamiento\/","title":{"rendered":"Enfermedad de Andrade: causan, s\u00edntomas y tratamiento"},"content":{"rendered":"<h4><span class=\"TextRun MacChromeBold SCXW70845588 BCX0\" lang=\"ES-MX\" xml:lang=\"ES-MX\" data-contrast=\"auto\"><span class=\"NormalTextRun SCXW70845588 BCX0\">La enfermedad de Andrade, tambi\u00e9n conocida como\u00a0<\/span><span class=\"NormalTextRun SCXW70845588 BCX0\">polineuropat\u00eda<\/span><span class=\"NormalTextRun SCXW70845588 BCX0\">\u00a0<\/span><span class=\"NormalTextRun SpellingErrorV2Themed SCXW70845588 BCX0\">amiloid\u00f3tica<\/span><span class=\"NormalTextRun SCXW70845588 BCX0\">\u00a0familiar (PAF) o\u00a0<\/span><span class=\"NormalTextRun SCXW70845588 BCX0\">amiloidosis<\/span><span class=\"NormalTextRun SCXW70845588 BCX0\">\u00a0hereditaria por\u00a0<\/span><span class=\"NormalTextRun SpellingErrorV2Themed SCXW70845588 BCX0\">transtirretina<\/span><span class=\"NormalTextRun SCXW70845588 BCX0\">\u00a0es un padecimiento hereditario causado por mutaciones en el gen de la\u00a0<\/span><span class=\"NormalTextRun SpellingErrorV2Themed SCXW70845588 BCX0\">transtirretina<\/span><span class=\"NormalTextRun SCXW70845588 BCX0\">, lo que puede provocar acumulaci\u00f3n de prote\u00ednas an\u00f3malas en nervios y \u00f3rganos.<\/span><\/span><span class=\"EOP SCXW70845588 BCX0\" data-ccp-props=\"{&quot;335551550&quot;:6,&quot;335551620&quot;:6}\">\u00a0<\/span><\/h4>\n<p><span data-contrast=\"auto\">La enfermedad de Andrade\u00a0o tambi\u00e9n\u00a0conocida\u00a0como\u00a0Polineuropat\u00eda\u00a0Amiloid\u00f3tica\u00a0Familiar de tipo I (PAF) es un trastorno degenerativo o progresivo,\u00a0que\u00a0por lo general, afecta principalmente al sistema nervioso perif\u00e9rico, el cual\u00a0est\u00e1\u00a0formado por los nervios y neuronas situados fuera del sistema nervioso central o SNC,\u00a0compuesto por el enc\u00e9falo y la m\u00e9dula espinal.\u00a0<\/span><span data-ccp-props=\"{&quot;335551550&quot;:6,&quot;335551620&quot;:6}\">\u00a0<\/span><\/p>\n<p><span data-contrast=\"auto\">Esta enfermedad neurodegenerativa, rara y grave afecta a aproximadamente 8.000 pacientes en todo el mundo y tiene su causa principal en una mutaci\u00f3n en el gen que codifica la prote\u00edna\u00a0transtiretina,\u00a0lo que puede provocar una acumulaci\u00f3n de\u00a0amiloide\u00a0en los tejidos del cuerpo, especialmente en los nervios, el coraz\u00f3n y los ri\u00f1ones y con el tiempo puede causar da\u00f1o a\u00a0dem\u00e1s \u00f3rganos.\u00a0<\/span><span data-ccp-props=\"{&quot;335551550&quot;:6,&quot;335551620&quot;:6}\">\u00a0<\/span><\/p>\n<p><span data-contrast=\"auto\">Por otro lado, dentro de los principales s\u00edntomas que puede desarrollar esta el presentar hormigueos o sensaci\u00f3n de entumecimiento, sudoraci\u00f3n anormal, fr\u00edo generalizado, alteraciones en el tr\u00e1nsito intestinal, n\u00e1useas, v\u00f3mitos, debilidad en general, disfunci\u00f3n er\u00e9ctil en hombres, cambios en la frecuencia card\u00edaca, problemas en el p\u00e1ncreas, anemia, retenci\u00f3n de l\u00edquidos e insuficiencia renal o reducci\u00f3n de la actividad de los ri\u00f1ones. Lamentablemente la gravedad de los s\u00edntomas tambi\u00e9n podr\u00eda empeorar a medida que la enfermedad va\u00a0avanzando.\u00a0\u00a0<\/span><span data-ccp-props=\"{&quot;335551550&quot;:6,&quot;335551620&quot;:6}\">\u00a0<\/span><\/p>\n<p><span data-contrast=\"auto\">La\u00a0enfermedad de Andrade es de car\u00e1cter gen\u00e9tico, es decir, se transmite de progenitores a hijos en cada generaci\u00f3n de forma dominante.\u00a0Por norma general, incluso los portadores desarrollan la patolog\u00eda en alg\u00fan momento de sus vidas.\u00a0Sin embargo, es posible que los descendientes se limiten a ser portadores sin llegar a padecer la enfermedad.<\/span><span data-ccp-props=\"{&quot;335551550&quot;:6,&quot;335551620&quot;:6}\">\u00a0<\/span><\/p>\n<p><span data-contrast=\"auto\">Su\u00a0diagnostico\u00a0tambi\u00e9n requiere de pruebas m\u00e9dicas, las cuales est\u00e1n centradas en temas gen\u00e9ticos que ayudan a identificar mutaciones en el gen de la\u00a0transtiretina\u00a0y tambi\u00e9n pueden realizarse pruebas de imagen y biopsias de los tejidos afectados para confirmar la presencia de\u00a0amiloide.<\/span><span data-ccp-props=\"{&quot;335551550&quot;:6,&quot;335551620&quot;:6}\">\u00a0<\/span><\/p>\n<p><span data-contrast=\"auto\">Actualmente, hay varios tratamientos disponibles para este padecimiento, entre los cuales destacan medicamentos que estabilizan la prote\u00edna\u00a0transtiretina\u00a0y reducen la producci\u00f3n de\u00a0amiloide. Tambi\u00e9n puede haber opciones de tratamiento para los s\u00edntomas espec\u00edficos de cada paciente, como la fisioterapia para problemas neurol\u00f3gicos y el manejo de la insuficiencia card\u00edaca y a pesar de que el diagn\u00f3stico precoz y su tratamiento han sido las principales\u00a0dificultades para los especialistas, se ha catalogado que la enfermedad es progresiva, irreversible y mortal, por lo que cuanto antes se empiece a tratar menor ser\u00e1 su progresi\u00f3n.<\/span><span data-ccp-props=\"{&quot;335551550&quot;:6,&quot;335551620&quot;:6}\">\u00a0<\/span><\/p>\n<p><img decoding=\"async\" src=\"https:\/\/elements-resized.envatousercontent.com\/envato-dam-assets-production\/EVA\/TRX\/86\/86\/e0\/a7\/03\/v1_E10\/E10DWDZ.jpg?w=800&amp;cf_fit=scale-down&amp;q=85&amp;format=auto&amp;s=a83be96beb02076bb7b3e2831089d2daaca4d1fd03143a4ff93c46391bc1ecbb\" \/><\/p>\n","protected":false},"excerpt":{"rendered":"<p>La enfermedad de Andrade, tambi\u00e9n conocida como\u00a0polineuropat\u00eda\u00a0amiloid\u00f3tica\u00a0familiar (PAF) o\u00a0amiloidosis\u00a0hereditaria por\u00a0transtirretina\u00a0es un padecimiento hereditario causado por mutaciones en el gen de la\u00a0transtirretina, lo que puede provocar acumulaci\u00f3n de prote\u00ednas an\u00f3malas en nervios y \u00f3rganos.\u00a0 La enfermedad de Andrade\u00a0o tambi\u00e9n\u00a0conocida\u00a0como\u00a0Polineuropat\u00eda\u00a0Amiloid\u00f3tica\u00a0Familiar de tipo I (PAF) es un trastorno degenerativo o progresivo,\u00a0que\u00a0por lo general, afecta principalmente al sistema nervioso [&hellip;]<\/p>\n","protected":false},"author":15,"featured_media":3844,"comment_status":"open","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[4624,6],"tags":[4679],"class_list":["post-3843","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-inovaccion-social","category-noticias","tag-enfermedad-de-andrade"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.8 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Enfermedad de Andrade: causan, s\u00edntomas y tratamiento - Historias que inspiran...<\/title>\n<meta name=\"description\" content=\"La enfermedad de Andrade, tambi\u00e9n conocida como\u00a0polineuropat\u00eda\u00a0amiloid\u00f3tica\u00a0familiar (PAF) o\u00a0amiloidosis\u00a0hereditaria\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" 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